ABSTRACT

Embryonal prostate sarcomas constitute less than 0.1% of primary prostate cancer cases in adults. Patients usually present with obstructive voiding and rectal compression symptoms. Due to the unusual aggressive behaviour of this disease, most patients presenting with advanced stage and metastatic le-sions will have a poor prognosis. We report a patient with rectal perforation in which pelvic exenteration was performed in order to reach negative sur-gical margins. In addition, severe rectal bleeding leading to acute blood loss supported the indication to perform this radical surgery in our case. Thus, every physician should keep this rare disease in mind during the differential diagnosis of a patient sharing clinical features with our case to reach an exa-ct diagnosis as soon as possible before metastatic disease develops