ABSTRACT

Familial Mediterranean fever (FMF) is an autosomal recessive disease, charac-terized by recurrent and selflimited attacks of fever, usually accompanied by polyserositis. The articular disease is the second most common manifestation after abdominal pain. The arthritis of FMF most frequently affecting the large joints of the lower extremities. Sacroiliitis due to FMF is very rare in children. Subcorneal pustular dermatosis (SPD), characterized by chronic, relapsing, pustular lesions. Although it usually occurs in middle-aged women, it is occa-sionally seen in childhood. There are various cutaneous manifestations of FMF but SPD and FMF association has been not previously described. In this report, we describe a 9- year-old girl who admitted to our hospital with fever, arthralgia and rash and diagnosed with sacroiliitis due to FMF and SPD.