ABSTRACT

Anomalous systemic arterial supply is a rare condition and it’s commonly seen in patients with Scimitar syndrome. A systemic arterial supply to a normal lung without anomaly is a rare variant of bronchopulmonary sequestration and it is characterized by normal pulmonary parenchymal tissue and bronchial connection. The lesion was classified by Pryce as type 1.Common clinical symptoms are chest pain, dyspnea, frequent lower respiratory infection, pulmonary hypertension, hemoptysis, and heart failure. The treatment may be surgical or transcatheter embolization. In this report we described a patient, a 6-year-old boy with Down syndrome and pulmonary hypertension, who had anomalous systemic artery supply to the left lower lob of the lung and its treatment with transcatheter closure by using a vascular plug II.