ABSTRACT

Lymphangioleiomyomatosis (LAM) is a disease occuring mainly in women and is characterised by smooth muscle cell proliferation. In this case report, a 27 year old woman with a complaint of cough and diagnosed with pulmo-nary LAM, renal angiomyolipoma, tuberousclerosis was presented. Thorax computed tomography of the patient, who had normal pulmonary function test, revealed bilateral multiple cysts and bilateral multiple renal angiomyoli-pomas. Lesions characterised with tuberousclerosis were detected in the cranium magnetic resonance. We aimed to present pulmonary LAM, which is an uncommon disease associated with renal angiomyolipoma and tuber-ousclerosis, with a review of the literature. (Gazi Med J 2011; 22: 52-5)