ABSTRACT

Dermatofibrosarcoma protuberans (DFSP) is a rare soft tissue tumor of dermis and subcutaneous tissue, mostly seen in trunk and extremities. Here we present a case of DFSP in the breast of a young women. A 26 years old female admitted to hospital with a 7 cm painless mass at right breast. Trucut biopsy reported spindle cell tumor. PET/CT and thorax CT revealed no metastases. Breast conserving surgery and sentinel lymph node biopsy was done. Pathological examination report was DFSP and reactive lymphadenopathy. Due to high recurrence rates in DFSP cases, wide local excision for acceptable oncologic margins and follow up is necessary.