ABSTRACT
Hyperimmunoglobulin E syndrome and botryomycosis are both uncommon disorders. This report describes the case of an 8 year old boy in whom these two disorders coexist, who presented with hypereosinophilia, and elevated im-munoglobulin E and was initially diagnosed as idiopathic hypereosinophilia. He was finally diagnosed as hyperim-munoglobulin E syndrome with the development of cutaneous and visceral botryomycosis under steroid treatment. (Gazi Med J 2011; 22: 124-6)